Ⅰ型瓜氨酸血症患儿肝移植术后并发乳糜漏的护理

doi:10.3761/j.issn.2096-7446.2025.07.014

中华急危重症护理杂志 ›› 2025, Vol. 6 ›› Issue (7): 850-852.doi: 10.3761/j.issn.2096-7446.2025.07.014

Ⅰ型瓜氨酸血症患儿肝移植术后并发乳糜漏的护理

谢仕龙(), 卢芳燕()

310003 杭州市浙江大学医学院附属第一医院肝移植中心（谢仕龙），护理部（卢芳燕）

收稿日期:2024-08-09 出版日期:2025-07-10 发布日期:2025-07-04
通讯作者: 卢芳燕 E-mail:584460871@qq.com;2196032@zju.edu.cn
作者简介:谢仕龙：男，本科，主管护师，E-mail：584460871@qq.com
基金资助:
浙江省医药卫生科技项目(2023KY105)

Nursing care of a child with citrullinemia type Ⅰ undergoing liver transplantation complicated with chylorrhea

XIE Shilong(), LU Fangyan()

Received:2024-08-09 Online:2025-07-10 Published:2025-07-04
Contact: LU Fangyan E-mail:584460871@qq.com;2196032@zju.edu.cn

摘要/Abstract

摘要：

总结1例Ⅰ型瓜氨酸血症患儿肝移植术后并发乳糜漏的护理体会。针对患儿曾因“高氨血症”急性发作导致精神异常、肝移植术后并发乳糜漏、他克莫司血药浓度难以调控、喂养困难等问题，采取组建多学科协作团队、预见性血氨管理、阶段性护理干预管理乳糜漏、精细化他克莫司药物护理、基于吮吸功能的喂养护理等措施。经过51 d的治疗与护理，患儿病情稳定出院。出院后随访6个月，患儿状况良好。

关键词: Ⅰ型瓜氨酸血症, 肝移植, 乳糜漏, 危重病护理, 儿科护理学

Abstract:

To summarize the nursing experience of a patient with citrullinemia type Ⅰ complicated by chylorrhea after liver transplantation. In view of the psychiatric disorders caused by acute episodes of “hyperammonemia" in the child，chylorrhea after liver transplantation，difficult control of tacrolimus blood concentration，feeding difficulties，and etc.，measures such as setting up multidisciplinary collaborative team，predictive management of blood ammonia，phased nursing intervention management of chylorrhea，refined tacrolimus nursing，feeding nursing based on sucking function were adopted. After 51 days of treatment and nursing，the patient was discharged from hospital in a stable condition. The patient was followed up for 6 months after discharge and was in good condition.

Key words: Citrullinemia Type Ⅰ, Liver Transplantation, Chylorrhea, Critical Care Nursing, Pediatric Nursing

谢仕龙, 卢芳燕. Ⅰ型瓜氨酸血症患儿肝移植术后并发乳糜漏的护理[J]. 中华急危重症护理杂志, 2025, 6(7): 850-852.

XIE Shilong, LU Fangyan. Nursing care of a child with citrullinemia type Ⅰ undergoing liver transplantation complicated with chylorrhea[J]. Chinese Journal of Emergency and Critical Care Nursing, 2025, 6(7): 850-852.

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Ⅰ型瓜氨酸血症患儿肝移植术后并发乳糜漏的护理

Nursing care of a child with citrullinemia type Ⅰ undergoing liver transplantation complicated with chylorrhea

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