Ⅰ型瓜氨酸血症患儿肝移植术后并发乳糜漏的护理

doi:10.3761/j.issn.2096-7446.2025.07.014

Abstract

Abstract:

To summarize the nursing experience of a patient with citrullinemia type Ⅰ complicated by chylorrhea after liver transplantation. In view of the psychiatric disorders caused by acute episodes of “hyperammonemia" in the child，chylorrhea after liver transplantation，difficult control of tacrolimus blood concentration，feeding difficulties，and etc.，measures such as setting up multidisciplinary collaborative team，predictive management of blood ammonia，phased nursing intervention management of chylorrhea，refined tacrolimus nursing，feeding nursing based on sucking function were adopted. After 51 days of treatment and nursing，the patient was discharged from hospital in a stable condition. The patient was followed up for 6 months after discharge and was in good condition.

Key words: Citrullinemia Type Ⅰ, Liver Transplantation, Chylorrhea, Critical Care Nursing, Pediatric Nursing

XIE Shilong, LU Fangyan. Nursing care of a child with citrullinemia type Ⅰ undergoing liver transplantation complicated with chylorrhea[J]. Chinese Journal of Emergency and Critical Care Nursing, 2025, 6(7): 850-852.

References 9

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Nursing care of a child with citrullinemia type Ⅰ undergoing liver transplantation complicated with chylorrhea

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