进行性家族性肝内胆汁淤积症患儿行亲体肝移植的术后护理

doi:10.3761/j.issn.2096-7446.2026.06.014

Abstract

Abstract:

To summarize the postoperative nursing experience of two children with progressive familial intrahepatic cholestasis who underwent parental liver transplantation. For children with severe cholestasis，persistent itching，malnutrition，and metabolic disorders，the nursing key points included establishing a dynamic monitoring system for cholestasis，strengthening comprehensive interventions for persistent skin itching，implementing individualized nutritional management plans，enhancing early identification and management of acute rejection reactions，implementing preventive care for metabolic bone disease. After active treatment and careful nursing，two children recovered after the surgery and were discharged from the hospital，the follow-up of more than 8~12 month showed good prognosis.

Key words: Cholestasis, Intrahepatic, Pediatric Nursing, Liver Transplantation, Intensive Care Units, Critical Care Nursing

WANG Yan, LU Fangyan, LIU Yuan, WANG Fang. Postoperative care of children with progressive familial intrahepatic cholestasis undergoing parental liver transplantation[J]. Chinese Journal of Emergency and Critical Care Nursing, 2026, 7(6): 714-716.

References 9

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Postoperative care of children with progressive familial intrahepatic cholestasis undergoing parental liver transplantation

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