法布雷病患者心脏移植的术后护理

doi:10.3761/j.issn.2096-7446.2023.03.013

Abstract

Abstract: The article summarized the postoperative nursing experience of a patient with Fabry disease undergoing heart transplantation. In view of the complex problems of patients' medical conditions and postoperative complications,measures such as circulatory goal-oriented management,implementing individualized enzyme replacement therapy,observing postoperative complications,and providing personalized rehabilitation plan were taken. On postoperative day 25,the patient was discharged in a stable condition.

Key words: Fabry, Enzyme Replacement Therapy, Heart Transplantation, Critical Care Nursing

YE Shaomei, CHEN Xia, YANG Qiaozhen. Postoperative care of heart transplantation for a patient with Fabry disease[J]. Chinese Journal of Emergency and Critical Care Nursing, 2023, 4(3): 255-257.

References

[1] Lenders M,Brand E.Mechanisms of neutralizing anti-drug antibody formation and clinical relevance on therapeutic efficacy of enzyme replacement therapies in fabry disease[J]. Drugs,2021,81(17):1969-1981.
[2] 中国法布雷病专家协作组. 中国法布雷病诊疗专家共识(2021年版)[J]. 中华内科杂志,2021,60(4):321-330.
China Fabry Disease Expert Collaborative Group. Expert consensus for diagnosis and treatment of Fabry disease in China (2021)[J]. Chin J Intern Med,2021,60(4):321-330.
[3] 姜江芬,孙雅逊,杨丽黎,等. 法布里病伴心肌肥厚及肾功能不全1例的护理[J]. 护理与康复,2021,20(3):49-51.
Jiang JF,Sun YX,Yang LL,et al.Nursing of 1 case of Fabry disease with cardiac hypertrophy and renal insufficiency[J]. J Nurs Rehabil,2021,20(3):49-51.
[4] 冯洁惠,徐建宁,王阳秭,等. 高龄患者紧急心脏移植的循证护理实践[J]. 中华急危重症护理杂志,2021,2(3):246-250.
Feng JH,Xu JN,Wang YZ,et al.Evidence-based nursing practice of emergency heart transplantation for an elderly patient[J]. Chin J Emerg Crit Care Nurs,2021,2(3):246-250.
[5] 罗桢蓝,龚静欢,朱凌燕. 心力衰竭患者液体管理的研究进展[J]. 中华护理杂志,2021,56(3):473-477.
Luo ZL,Gong JH,Zhu LY.Research progress of fluid management strategies in patients with heart failure[J]. Chin J Nurs,2021,56(3):473-477.
[6] 李东燕,蒋美丹,赵莹,等. 1例注射用阿加糖酶β治疗儿童法布里病的护理[J]. 浙江医学,2021,43(8):896-897.
Li DY,Jiang MD,Zhao Y,et al.Care of children with Fabry disease[J]. Zhejiang Med J,2021,43(8):896-897.
[7] 曾妃,梁江淑渊,兰美娟. 1例肝肺联合移植术后患者的护理[J]. 中华护理杂志,2021,56(10):1540-1543.
Zeng F,Liang JSY,Lan MJ.Nursing care of 1 patient after combined liver and lung transplantation[J]. Chin J Nurs,2021, 56(10):1540-1543.
[8] 褚君卿,高春华,俞超,等. 肺移植患者围手术期营养支持的研究进展[J]. 中华急危重症护理杂志,2021,2(4):360-364.
Chu JQ,Gao CH,Yu C,et al.Research progress of perioperative nutritional support for patients with lung transplantation[J]. Chin J Emerg Crit Care Nurs,2021,2(4):360-364.
[9] 刘娅桐,蔡忠香,方婷. 心脏移植术后患者康复运动的研究进展[J]. 中华现代护理杂志,2021,27(29):3928-3932.
Liu YT,Cai ZX,Fang T.Progress in the rehabilitation exercise of patients after heart transplantation[J]. Chin J Mod Nurs,2021,27(29):3928-3932.
[10] Shemesh Y,Peles-Bortz A,Peled Y,et al.Feelings of indebtedness and guilt toward donor and immunosuppressive medication adherence among heart transplant(HTx）patients,as assessed in a cross-sectional study with the Basel Assessment of Adherence to Immunosuppressive Medications Scale(BAASIS)[J]. Clin Transplant,2017,31(10):e13053.

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Postoperative care of heart transplantation for a patient with Fabry disease

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