儿童脑型肾上腺脑白质营养不良行造血干细胞移植的护理

doi:10.3761/j.issn.2096-7446.2023.05.012

Abstract

Abstract: To summarize the nursing experience of 2 children with adrenoleukodystrophy undergoing hematopoietic stem cell transplantation. According to their characteristics of progressive motor and swallowing function deterioration,and malnutrition after hematopoietic stem cell transplantation,a multidisciplinary treatment and nursing team was established to carry out nutritional risk screening and evaluation as soon as possible. We observed the changes of the disease closely,and identified the complications such as intestinal graft-versus-host disease and delayed hemorrhagic cystitis as early as possible,gave psychological support to children and parents to relieve anxiety. Individualized rehabilitation exercise and multidisciplinary joint follow-up plan was made to promote the early recovery of diseases. After careful treatment and nursing,2 children were discharged from hospital with normal bone marrow function.

Key words: Child, Adrenoleukodystrophy, Hematopoietic Stem Cell Transplantation, Critical Care Nursing

ZHOU Hongqin, CHEN Xiuping, ZHU Jihua, ZHANG Chaolang, CHEN Xiaofei, CHE Yueping. Nursing care of children with adrenalleukodystrophy undergoing hematopoietic stem cell transplantation[J]. Chinese Journal of Emergency and Critical Care Nursing, 2023, 4(5): 444-446.

References

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Nursing care of children with adrenalleukodystrophy undergoing hematopoietic stem cell transplantation

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