马凡综合征并发恶性心律失常患者行血管外植入型心律转复除颤器治疗的护理

doi:10.3761/j.issn.2096-7446.2026.09.012

Abstract

Abstract:

To summarizes the perioperative nursing experience of a patient with Marfan syndrome complicated with malignant arrhythmia undergoing implantation of an extravascular implantable cardioverter defibrillator（EV-ICD）. Key nursing points included malignant arrhythmia risk management and preoperative education，integrated symptom-monitoring-device event surveillance，prevention and management of postoperative complications，comprehensive perioperative rehabilitation，targeted psychological interventions，and promotion of proactive health behaviors. Following multidisciplinary treatment and comprehensive nursing care，the patient recovered well and was discharged after a 31-day hospital stay. At the 1-month follow-up，no recurrence of malignant arrhythmias or device-related complications was observed，and the patient’s level of proactive health behaviors had promoted significantly.

Key words: Marfan Syndrome, Malignant Arrhythmia, Implantable Cardioversion Defibrillator, Nursing Care

HUANG Dandan, ZHU Shuting, CHEN Xi, SONG Jianping. Nursing care for a patient with Marfan syndrome complicated by malignant arrhythmia undergoing extravascular implantable cardioversion defibrillator therapy[J]. Chinese Journal of Emergency and Critical Care Nursing, 2026, 7(9): 1104-1107.

References 9

[1]	Connolly HM, Niaz T, Bowen JM. What is Marfan syndrome[J]. Jama, 2023, 329(18):1618. doi: 10.1001/jama.2023.3826
[2]	Spittler R, Salzbrunn T, Metzner A, et al. Ventricular dispersion and repolarization in Marfan syndrome:a clinical analysis[J]. Heart Rhythm O2,2025, 6(10):1638-1645.
[3]	Friedman P, Murgatroyd F, Boersma LVA, et al. Performance and safety of the extravascular implantable cardioverter defibrillator through long-term follow-up:final results from the pivotal study[J]. Circulation, 2025, 151(4):322-332. doi: 10.1161/CIRCULATIONAHA.124.071795
[4]	Demolder A, von Kodolitsch Y, Muiño-Mosquera L, et al. Myocardial function,heart failure and arrhythmia in Marfan syndrome:a systematic literature review[J]. Diagnostics, 2020, 10(10):751. doi: 10.3390/diagnostics10100751
[5]	Blomström-Lundqvist C, Traykov V, Erba PA, et al. European Heart Rhythm Association(EHRA) international consensus document on how to prevent,diagnose,and treat cardiac implantable electronic device infections:endorsed by the Heart Rhythm Society(HRS),the Asia Pacific Heart Rhythm Society(APHRS),the Latin American Heart Rhythm Society(LAHRS),International Society for Cardiovascular Infectious Diseases(ISCVID),and the European Society of Clinical Microbiology and Infectious Diseases(ESCMID) in collaboration with the European Association for Cardio-Thoracic Surgery(EACTS)[J]. Eur Heart J, 2020, 41(21):2012-2032. doi: 10.1093/eurheartj/ehaa010 pmid: 32101604
[6]	张一非, 李梅, 黄丹丹. 急性心肌梗死并发心力衰竭后心搏骤停患者的心脏康复护理[J]. 中华急危重症护理杂志, 2024, 5(5):439-442.
	Zhang YF, Li M, Huang DD. Cardiac rehabilitation nursing care of a patient who suffered a cardiac arrest following acute myocardial infarction and complicated acute heart failure[J]. Chin J Emerg Crit Care Nurs, 2024, 5(5):439-442.
[7]	Singer P, Blaser AR, Berger MM, et al. ESPEN practical and partially revised guideline:Clinical nutrition in the intensive care unit[J]. Clin Nutr, 2023, 42(9):1671-1689. doi: 10.1016/j.clnu.2023.07.011
[8]	Chen LK, Woo J, Assantachai P, et al. Asian working group for sarcopenia:2019 consensus update on sarcopenia diagnosis and treatment[J]. J Am Med Dir Assoc, 2020, 21(3):300-307.e2. doi: 10.1016/j.jamda.2019.12.012
[9]	Panetta M, Bianchetti A, Udugampolage NS, et al. Discussing psychological and psychotherapeutic support for patients with Marfan syndrome(MFS) and their family:an example of a structured program in Italy[J]. Front Psychol, 2023, 14:1176692. doi: 10.3389/fpsyg.2023.1176692

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Nursing care for a patient with Marfan syndrome complicated by malignant arrhythmia undergoing extravascular implantable cardioversion defibrillator therapy

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