Abstract: The nursing experience of a child with propionic acidemia complicated with status epilepticus was summarized. According to the characteristics of the urgent onset and rapid progress of this case,specimens were collected in time to strengthen the dynamic observation of the child's condition. Key points of nursing also included emergency care for epileptic seizures;nutrition screening and assessment,proper protein consume and maintenance of water,electrolyte and acid-base balance;early observation and prevention of hyperammonemia encephalopathy;observation and prevention of hypoglycemia;guide of family emergency management. After 8 days of active treatment and careful nursing,the patient's condition was controlled and discharged. The parents were followed up by telephone for 2 years,and the child's condition was stable.

Key words: Infant, Propionic Acidemia, Status Epilepticus, Emergency Nursing