总结1例家族性高胆固醇血症患儿行多米诺肝移植术后并发急性肝动脉血栓的急救护理体会。 针对肝动脉血栓早期临床症状不典型，溶栓治疗过程中极易发生出血、感染等问题，采取加强肝动脉血栓形成的早期识别，实施导管接触性溶栓治疗专人管理，精准化抗凝管理，持续性低负压腹腔冲洗，制订个体化营养管理方案及皮肤黄色瘤护理方案。 经积极治疗与护理，患儿病情稳定，顺利出院，随访4个月，情况良好。

To summarize the first aid and nursing experience on early hepatic artery thrombosis of domino liver transplantation for a child with familial hypercholesterolemia. In order to solve the problems of atypical early clinical symptoms of hepatic artery thrombosis，easy occurrence of bleeding and infection during thrombolytic therapy，we adopted measures such as early identification of hepatic artery thrombosis，special management of catheter contact thrombolytic therapy，precise anticoagulation management，continuous low negative pressure abdominal irrigation，individualized nutrition management and skin management of xanthoma. After active treatment and meticulous care，the child was stable and discharged from the hospital and followed up for more than 4 months，with a good prognosis.