ISSN 2097-6046（网络）
ISSN 2096-7446（印刷）
CN 10-1655/R
主管：中国科学技术协会
主办：中华护理学会
中华急危重症护理杂志

中华急危重症护理杂志 ›› 2026, Vol. 7 ›› Issue (8): 966-968.doi: 10.3761/j.issn.2096-7446.2026.08.011

• 急症护理研究 • 上一篇    下一篇

扩张型心肌病并发心室电风暴患儿的风险识别及护理

朱建美(), 林敏, 杨小敏, 丁亚平*()   

  1. 浙江大学医学院附属儿童医院心血管内科/儿童少年健康与疾病国家临床医学研究中心 杭州市 310052
  • 收稿日期:2026-02-12 出版日期:2026-08-10 发布日期:2026-08-04
  • 通讯作者: *丁亚平，E-mail：6518147@zju.edu.cn
  • 作者简介:朱建美：女，本科，主管护师，护士长，E-mail：6202032@zju.edu.cn
    作者贡献声明

    朱建美：论文撰写；林敏：病历资料收集、整理；杨小敏：文献查询；丁亚平：论文指导、修改

  • 基金资助:
    浙江省教育厅项目(Y202559858)

Risk identification and nursing care of a child with dilated cardiomyopathy complicated by ventricular electrical storm

ZHU Jianmei(), LIN Min, YANG Xiaomin, DING Yaping*()   

  1. Department of Cardiology， Children’s Hospital，Zhejiang University School of Medicine/National Clinical Research Center for Children and Adolescents’ Health and Diseases， Hangzhou 310052， China
  • Received:2026-02-12 Online:2026-08-10 Published:2026-08-04
  • Contact: *DING Yaping，E-mail：6518147@zju.edu.cn
  • Supported by:
    Zhejiang Provincial Department of Education Project(Y202559858)

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摘要：

总结1例基因突变致扩张型心肌病并发心室电风暴患儿多策略治疗的急救护理体会。针对患儿发生心室电风暴、猝死风险极高的特点，实施以下护理措施：①心室电风暴的多参数动态预警与应急响应；②体外膜肺氧合治疗期间持续监测患儿的循环状态、组织灌注与心肌电的稳定性；③心脏再同步治疗除颤器植入后持续监测患儿心律；④经心外膜射频消融治疗期间的风险管理；⑤医疗相关创伤反应的评估及个体化心理干预；⑥经心外膜射频消融治疗患儿出院后的动态风险识别及连续性护理。患儿住院第62天出院，恶性心律失常得到控制，出院后随访病情稳定。

关键词: LMNA基因突变, 心室电风暴, 心脏再同步治疗除颤器, 射频消融, 急救护理

Abstract:

To summarize the emergency nursing experience of a child with dilated cardiomyopathy caused by a gene mutation complicated by ventricular electrical storm undergoing multi-strategy therapy. Given the extremely high risk of ventricular electrical storm and sudden cardiac death，the key nursing measures included multi-parameter dynamic early warning and emergency response for ventricular electrical storm；continuous monitoring of circulatory status，tissue perfusion，and myocardial electrical stability during extracorporeal membrane oxygenation therapy；continuous monitoring of the child’s heart rhythm after cardiac resynchronization therapy defibrillator implantation；risk management during epicardial radiofrequency ablation therapy；assessment of medical-related traumatic reactions and individualized psychological intervention；dynamic risk identification and continuous care for children after epicardial radiofrequency ablation therapy. The patient was discharged after 62 days of hospitalization，and the malignant arrhythmia was controlled. After discharge，the condition remained stable during follow-up.

Key words: LMNA Gene Mutation, Ventricular Electrical Storm, Cardiac Resynchronization Therapy Defibrillator, Radiofrequency Ablation, Emergency Nursing