The postoperative nursing experience of two children with propionic acidemia undergoing parent-child liver transplantation was summarized. In view of the problems of multiple organ involvements,metabolic disorders,vascular complications and difficulty of sedation in this group of children,the following interventions were adopted,including monitoring the function of important organs and reporting abnormal conditions timely,the maintain of acid-base balance and being cautious of acidosis and hyperammonemia,strict implementation of anticoagulation therapy to reduce vascular-related complications,effective sedative care to prevent the occurrence of convulsions,accurate administration of immunosuppressants to prevent acute rejection,special formulated diets and control of protein intake. After active treatment and meticulous care,two children were discharged from the hospital after surgery and followed up for more than 1 year with a good prognosis.
WANG Yan
,
LU Fangyan
,
WANG Fang
. Postoperative nursing of children with propionic acidemia undergoing parent-child liver transplantation[J]. Chinese Journal of Emergency and Critical Care Nursing, 2023
, 4(4)
: 347
-349
.
DOI: 10.3761/j.issn.2096-7446.2023.04.014
[1] 陳慧儀,万平,夏强. 肝移植治疗甲基丙二酸血症和丙酸血症的研究进展[J]. 国际消化病杂志,2020,40(2):75-77,86.
Chen HX,Wan P,Xia Q.Research progress of liver transplantation in treatment of methylmalonic acidemia and propionic acidemia[J]. Int J Dig Dis,2020,40(2):75-77,86.
[2] 罗毅. 中国儿童肝移植操作规范(2019版)[J]. 中华移植杂志(电子版),2019,13(3):181-186.
Luo Y.Technical specification for pediatric liver transplantation in China(2019 edition)[J]. Chin J Transplant Electron Ed,2019,13(3):181-186.
[3] 王燕,卢芳燕,汤洒潇. 6例终末期肝病合并先天性心脏病患儿行肝移植的术后护理[J]. 中华护理杂志,2021,56(10):1544-1548.
Wang Y,Lu FY,Tang SX.Postoperative nursing care of 6 children with end-stage liver disease combined with congenital heart disease undergoing liver transplantation[J]. Chin J Nurs,2021,56(10):1544-1548.
[4] 中国研究型医院学会加速康复外科专业委员会. 儿童肝移植围手术期管理专家共识[J]. 中华外科杂志,2021,59(3):179-191.
Enhanced Recovery after Surgery Committee of Chinese Research Hospital Association. Expert consensus of perioperative management in pediatric liver transplantation[J]. Chin J Surg,2021,59(3):179-191.
[5] 曾妃,沈婷芳,陈晨. 丙酸血症患儿行活体肝移植术后的护理经验[J]. 护理与康复,2021,20(8):63-65.
Zeng F,Shen TF,Chen C.Nursing experience after living donor liver transplantation in children with propionic acidemia[J]. J Nurs Rehabil,2021,20(8):63-65.
[6] 王芳,卢芳燕. 1例鸟氨酸氨甲酰基转移酶缺乏症患儿行肝移植的围手术期护理[J]. 中华护理杂志,2022,57(13):1618-1622.
Wang F,Lu FY.Perioperative nursing care of a child with otrnithine transcarbamlase deficiency undergoing liver transplantation[J]. Chin J Nurs,2022,57(13):1618-1622.
[7] 张婉莹,戴燕红,金花,等. 儿童镇静程度评估工具的研究进展[J]. 中华护理杂志,2021,56(11):1644-1648.
Zhang WY,Dai YH,Jin H,et al.Research progress of assessment tools for the level of pediatric sedation[J]. Chin J Nurs,2021,56(11):1644-1648.
