eISSN 2097-6046
ISSN 2096-7446
CN 10-1655/R
Responsible Institution：China Association for Science and Technology
Sponsor：Chinese Nursing Association
中华急危重症护理杂志

Chinese Journal of Emergency and Critical Care Nursing >

2026 , Vol. 7 >Issue 8: 982 - 985

DOI: https://doi.org/10.3761/j.issn.2096-7446.2026.08.016

Critical Care Research

Pulmonary rehabilitation nursing for a patient with myofibrillar myopathy caused by a BAG3 gene mutation who had difficulty weaning from mechanical ventilation

  • MA Yanxin ,
  • WANG Guoying ,
  • HU Yuding ,
  • LIU Huiling
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  • 1 Intensive Care Unit， the Second Hospital of Hebei Medical University， Shijiazhuang 050000， China
    2 Nursing Department， the Second Hospital of Hebei Medical University， Shijiazhuang 050000， China
*LIU Huiling，E-mail：26900555@hebmu.edu.cm

Received date: 2025-08-14

  Online published: 2026-08-04

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Abstract

To summarize the experience of pulmonary rehabilitation nursing for a patient with myofibrillar myopathy caused by BAG3 gene mutation who had difficulty in weaning from mechanical ventilation. In response to the muscle weakness and respiratory muscle involvement caused by this rare disease，as well as the patient’s anxiety and depression issues，a multidisciplinary team was established to develop and implement an early activity plan centered on four-level movement，staged weaning training，personalized diaphragm exercise under ultrasound guidance，and psychological intervention incorporating positive psychology theories. After 33 days of systematic pulmonary rehabilitation nursing，the patient successfully weaned off mechanical ventilation and was discharged smoothly.

Key words： Myofibrillar Myopathy; Mechanical Ventilation; Pulmonary Rehabilitation; Early Mobilization; Critical Care Nursing

Cite this article

MA Yanxin , WANG Guoying , HU Yuding , LIU Huiling . Pulmonary rehabilitation nursing for a patient with myofibrillar myopathy caused by a BAG3 gene mutation who had difficulty weaning from mechanical ventilation[J]. Chinese Journal of Emergency and Critical Care Nursing, 2026 , 7(8) : 982 -985 . DOI: 10.3761/j.issn.2096-7446.2026.08.016

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