总结1例面部起病的感觉运动神经元病患者的护理体会。护理要点：针对该例患者Ⅱ型呼吸衰竭的特点采取多学科团队协作,应用无创通气纠正呼吸衰竭;精准评估吞咽功能,做好进食后的口腔清洁,落实预防误吸、窒息等措施,以应对患者拒绝留置胃管可能导致的误吸等风险;针对疾病的罕见性及患者对疾病的错误认知、焦虑情绪,提供个性化清单式健康教育,指导患者积极应对疾病;提供“互联网+”线上服务,进行长期的随访管理。经过7 d的精心护理,患者症状改善出院,出院后随访3个月,患者症状稳定,无误吸、吸入性肺炎等不良事件发生。
To summarize the nursing care experience for a patient with facial onset sensory and motor neuronopathy. According to the characteristics of type Ⅱ respiratory failure in this patient,multi-disciplinary team cooperation was adopted and noninvasive ventilator was used to correct respiratory failure. Nurses accurately evaluated swallowing function,did a good job in oral hygiene after eating,and implemented measures to prevent aspiration and asphyxia,so as to deal with the risk of aspiration and other risks that may be caused because the patient refused to retain a gastric tube. In view of the rarity of the disease and the patient's wrong cognition and anxiety about the disease,nurses provided personalized list health education,guided the patient to actively deal with the disease. Internet plus online service was also provided for long-term follow-up management. After 7 days of careful nursing,the patient's symptoms were improved and discharged. After 3 months of follow-up after discharge,the patient's symptoms were stable,and there were no adverse events such as aspiration and aspiration pneumonia.
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