总结1例基因突变致扩张型心肌病并发心室电风暴患儿多策略治疗的急救护理体会。针对患儿发生心室电风暴、猝死风险极高的特点，实施以下护理措施：①心室电风暴的多参数动态预警与应急响应；②体外膜肺氧合治疗期间持续监测患儿的循环状态、组织灌注与心肌电的稳定性；③心脏再同步治疗除颤器植入后持续监测患儿心律；④经心外膜射频消融治疗期间的风险管理；⑤医疗相关创伤反应的评估及个体化心理干预；⑥经心外膜射频消融治疗患儿出院后的动态风险识别及连续性护理。患儿住院第62天出院，恶性心律失常得到控制，出院后随访病情稳定。

To summarize the emergency nursing experience of a child with dilated cardiomyopathy caused by a gene mutation complicated by ventricular electrical storm undergoing multi-strategy therapy. Given the extremely high risk of ventricular electrical storm and sudden cardiac death，the key nursing measures included multi-parameter dynamic early warning and emergency response for ventricular electrical storm；continuous monitoring of circulatory status，tissue perfusion，and myocardial electrical stability during extracorporeal membrane oxygenation therapy；continuous monitoring of the child’s heart rhythm after cardiac resynchronization therapy defibrillator implantation；risk management during epicardial radiofrequency ablation therapy；assessment of medical-related traumatic reactions and individualized psychological intervention；dynamic risk identification and continuous care for children after epicardial radiofrequency ablation therapy. The patient was discharged after 62 days of hospitalization，and the malignant arrhythmia was controlled. After discharge，the condition remained stable during follow-up.