总结1例巨膀胱-小结肠-肠蠕动不良综合征患儿的营养支持护理体会。针对该病严重的肠道消化吸收障碍,易致营养不良和肠功能衰竭,依赖肠外营养,营养支持是其护理难点。护理要点：动态评估营养状况,为制订营养治疗方案提供依据;选择合理营养支持途径,进行肠外营养和肠内营养支持;给予对症支持护理,避免严重并发症;建立长期随访机制,开展健康教育,改善疾病预后。经过45 d规范治疗及护理,患儿病情得到控制,体重较前增长,稳定后出院继续定期随访。
To summarize nutritional support care of a child with megacystis microcolon intestinal hypoperistalsis syndrome. In terms of the serious intestinal digestion and absorption disorder,it was easy to cause malnutrition and intestinal failure,and it was dependent on parenteral nutrition,nutritional support was the difficulty of the nursing. Dynamical evaluation of nutritional status was adopted to provide a basis for formulating nutritional treatment plans. Reasonable nutritional support method was selected,and parenteral nutrition and enteral nutrition support were provided. Symptomatic supportive care was provided to avoid serious complications. And long-term follow-up mechanisms were established to carry out health education and improve disease prognosis. After 45 days of standardized treatment and care,the child's condition was controlled,with increased weight. After stabilization,he was discharged from the hospital and continued to be followed up regularly.
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