总结1例普拉德-威利综合征患儿肺部感染继发脓毒性休克的护理体会。针对患儿脓毒症性休克进展迅速,呼吸道分泌物难以有效清除,用药复杂,易出现并发症等棘手问题,护理要点：应用特异性指标有效识别休克征象,医护紧密配合抢救;肺泡灌洗联合肺部超声引导胸部物理治疗清除分泌物,促进肺复张;准确用药,严密监测药物疗效与副作用;预防压力性损伤与急性肾损伤。经过30 d的精心治疗与护理,患儿病情稳定出院,门诊随访恢复良好。
To summarize the nursing experience of a child with Prader-Willi syndrome complicated with pulmonary infection and secondary septic shock. In view of the rapid progress of septic shock in children,difficulty to effectively remove respiratory secretions,complicated medication,and being prone to complications,nursing points included：the application of specific indicators to effectively identify the signs of shock and close cooperation for rescue between doctors and nurses; bronchoalveolar lavage combined with lung ultrasound to guide chest physical therapy to remove secretions and promote lung recruitment; accurate medication,close monitoring of drug efficacy and side effects; prevention of pressure injury and acute kidney injury. After 30 days of careful treatment and care,the child was discharged in stable condition and recovered well during outpatient follow-up.
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