总结1例兰尼碱受体2基因变异相关儿茶酚胺敏感性多形性室性心动过速并发心搏骤停患儿的护理体会。针对该患儿缺血缺氧时间长、病情进展迅速、反复恶性心律失常及高敏感性情绪反应等护理难点，快速启动个体化目标温度管理，实施体外膜肺氧合联合俯卧位通气治疗，及早识别恶性心律失常，迅速激活应急响应系统，采取多维度情绪刺激规避策略，减少恶性心律失常事件发生，同时早期开展渐进性运动康复。经过31 d精心护理，患儿顺利转外院行康复治疗，随访近6个月，未再发生恶性心律失常。

To summarize the nursing experience of a child with ryanodine receptor 2 gene variant-related catecholaminergic polymorphic ventricular tachycardia complicated with cardiac arrest. Given the nursing challenges of prolonged ischemic hypoxia，rapid disease progression，recurrent malignant arrhythmia，and highly sensitive emotional stimuli in this pediatric patient，we implemented rapid initiation of individualized high-quality targeted temperature management，conducted extracorporeal membrane oxygenation combined with prone ventilation therapy，promptly identified malignant arrhythmia，quickly activated the emergency response system，adopted multidimensional emotional stimulus avoidance strategies to reduce malignant arrhythmia episodes，while initiating progressive motor rehabilitation early. After 31 days of meticulous nursing，the child was successfully transferred to another hospital for rehabilitation therapy. During the 6-month follow-up period，no further malignant arrhythmia events occurred.